atpolt.blogg.se

• #Pierre robin sequence adults series#

This rare cleft condition is separated from the eponymous term Pierre Robin Syndrome, which Robin had at first termed “Le Grand Syndromie du Glossoptosis”, and that was originally meant to describe the simple combined local and systemic effects of mandibular hypoplasia innately associated with glossoptosis. In honor of Pierre Robin, who had also seen and first described this rare type of cleft in neonates with extremely small lower jaws, Poswillo proposed the term Pierre Robin sequence as posthumously named after him. Later in the 1960s, authors writing in British Oral Surgery journals, and in particular David Poswillo, a New Zealand Oral & Maxillofacial Surgeon and UK based teratologist, postulated that the combination of am extremely small mandible, and oligohydramnios during late pregnancy, combined to produce a particularly unique form of non-formation of the palatal shelf - a condition distinct from other more usual forms of cleft palate. He is credited with recognizing that lying at-risk babies on their backs potentiated upper airway obstruction - by choking on the “fallen tongue” and his advice of prone (tummy lying) sleeping and feeding techniques were widely adopted in France and internationally at the time. In newborns, and young children he pioneered the understanding of the effects of small jaws as beginning from birth, and how the condition of glossoptosis may also lead to spontaneous or unexpected infant fatality during sleep, or what is now considered as cot death or Sudden Infant Death Syndrome.

#Pierre robin sequence adults series#

In a series of articles, Robin demonstrated that in adults, small mandibles lead to a series of both local dental and malocclusion effects, as well as wider systemic medical problems, including the development of what came to be known as Obstructive Sleep Apnoea. This invention predated the eventual development of mandibular advancement splints used by dentists in sleep medicine today. Robin proposed a novel idea of holding the lower jaw forward and mouth open, through the use of special dental splints and specifically with an invented and novel device he later called the "Monobloc". His first papers described clinical observations in young adults who had small jaws, and who also had upper airway obstruction during sleep. In a series of articles, beginning in 1923, Robin described the combined condition of underdevelopment of the mandible and retraction of the tongue. He was professor at the French School of Stomatology, and from 1914, he was editor-in-chief of the Revue de Stomatologie. Pierre Robin ( French: 1866–1950) was a French stomatologist ( dental surgeon) from Paris. French dental surgeon who first described Pierre Robin sequence